ISSN: 2155-6148
+44 1223 790975
Swati Chhabra
India
Case Report
Dexmedetomidine: A Saviour in a Child with Hand Schuller Christian Disease
for MRI
Author(s): Geeta Ahlawat, Savita Saini, Swati Chhabra, Amita Singh, Kirti Kshetrapal and Jaswant Singh
Geeta Ahlawat, Savita Saini, Swati Chhabra, Amita Singh, Kirti Kshetrapal and Jaswant Singh
Hand Schuller Christian disease (HSC) primarily affects infants and children. Its classical presentation includes triad of exophthalmos, diabetes insipid us, and calvariallytic lesions. Systemic involvement may include hepatomegaly, lymphadenopathy, dermatological, gastrointestinal tract, renal, pulmonary and CNS involvement. CNS involvement includes convulsions, increased intracranial pressure, focal neurological deficits, mental retardation, hearing disturbance, and tremors. We encountered a 4 year old female child with HSC disease who was posted for elective MRI scan under anaesthesia. Patient’s history, physical examination, and lab reports revealed multitude of problems enumerated in case report. Such patients when posted for anaesthesia pose a major challenge in view of multiple organ involvement. Polydipsia made difficult to keep the patient fasting and g.. View More»
DOI:
10.4172/2155-6148.1000683