Journal of Hematology & Thromboembolic Diseases
Open Access

Department of Pediatrics, University of Saskatchewan, Saskatoon, Saskatchewan, Canada

Publications

• Case Report   
  Acute Soft Head Syndrome in Sickle Cell Anemia: Creating a Firm Approach
  Author(s): Mark Drew*, Derek Fladeland and Roona Sinha
  
  Sickle Cell Disease (SCD) is the most common inherited disease worldwide and presents with a myriad of complications. A rare complication of SCD is Acute Soft Head Syndrome (ASHS). We present the case of a 14-year-old male with homozygous sickle cell anemia (HbSS) who presented with Vaso-Occlusive Crisis (VOC) complicated by the peculiar development of a scalp mass. Magnetic Resonance Imaging (MRI) showed calvarium changes consistent with ASHS. Current literature lacks standardized management for such a complication. As such, we outline recommendations for imaging modalities, therapeutic interventions, and ongoing management based on this patient’s course over two years... View More»
  DOI: 10.35248/2329-8790.23.11.535

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