ISSN: 2155-6148
Dr, Department of Anesthesia, Kyoto University Hospital, Kyoto, Japan
Dr. Shuji Kawamoto is an Associate professor in the Department of Anesthesia, Kyoto University Hospital, Kyoto, Japan. Dr.Shuji Kawamoto is the author/editors/reviewer in several international journals. He published articles in many journals and the articles are informative and got good citations.
Case Report
Perioperative Management of Brain-Dead Bilateral Lung Transplantation in a Patient with Kartagener Syndrome: A Case Report
Author(s): Shuji Kawamoto*, Atsuko Shiraki, Chikashi Takeda, Tomoharu Tanaka and Kazuhiko Fukuda
Background: Kartagener syndrome (KS) is a partial disease of primary ciliary dyskinesia with defects in the fine
structure of cilia and flagella. KS is an autosomal recessive inherited disease with three major features: visceral
inversion, chronic sinusitis, and bronchiectasis. Lung transplantation is an option for end-stage KS, which results in
respiratory insufficiency. However, there have been few reports on perioperative management of lung transplantation
in patients with KS.
Case presentation: A 44-year-old female who was diagnosed with KS in infancy had tracheotomy at age 42 to prevent
infection, and was placed on standby for lung transplantation under a ventilator. After a two-year wait, she underwent
bilateral brain-dead lung transplantation. In parallel with induction of anesthesia, the left femoral artery and vein
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DOI:
10.35248/2155-6148.20.11.968