ISSN: 2155-6148
Department of Anesthesia, Kyoto University Hospital, Kyoto, Japan
Case Report
Perioperative Management of Brain-Dead Bilateral Lung Transplantation in a Patient with Kartagener Syndrome: A Case Report
Author(s): Shuji Kawamoto*, Atsuko Shiraki, Chikashi Takeda, Tomoharu Tanaka and Kazuhiko Fukuda
Background: Kartagener syndrome (KS) is a partial disease of primary ciliary dyskinesia with defects in the fine
structure of cilia and flagella. KS is an autosomal recessive inherited disease with three major features: visceral
inversion, chronic sinusitis, and bronchiectasis. Lung transplantation is an option for end-stage KS, which results in
respiratory insufficiency. However, there have been few reports on perioperative management of lung transplantation
in patients with KS.
Case presentation: A 44-year-old female who was diagnosed with KS in infancy had tracheotomy at age 42 to prevent
infection, and was placed on standby for lung transplantation under a ventilator. After a two-year wait, she underwent
bilateral brain-dead lung transplantation. In parallel with induction of anesthesia, the left femoral artery and vein
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DOI:
10.35248/2155-6148.20.11.968