Pediatrics & Therapeutics
Open Access

A child with malignant ovarian tumor and Mayer Rokitanisky Kuster Hauser (MRKH) syndrome

International Conference and Exhibition on Pediatric Oncology and Clinical Pediatrics

August 11-13, 2016 Toronto, Canada

Getnet Tesfaye Yihunie, Bazezew Fekad, Amsalu Worku and Wassihun Nega

Bahirdar University, Ethiopia

Posters & Accepted Abstracts: Pediat Therapeut

Abstract :

Background: Ovarian tumors occur in an estimated 2.6/100,000 girls per year, excluding functional lesions. 10 to 20% are malignant and they represent 3% of cancers in girls under the age of 15. Ovarian cancer is rare in childhood. This explains why there are only scattered reports on it in the literature and why there is a lack of specific pediatric treatment. Congenital anomalies of the Mullerian system are common defects, reported in up to 3.2% of all women. Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome, the most severe anomaly of Mullerian system, characterized by absent vagina and uterus congenitally, both ovaries are of normal size and fallopian tubes are normal; rudimentary uterine horns may be present in this syndrome. Case: A 12 years old child comes with abdominal swelling of 4weeks and worsening of abdominal pain for 2 weeks. It does not start menarche. She is admitted with acute abdomen due to ovarian tumor torsion. Further diagnosis modality, management and patient outcome will be discussed during the presentation. Conclusion: The diagnosis of ovarian tumors in pediatrics is often difficult and delayed because of non-specific symptoms and diverse presentations on imaging. Concurrent association of pelvic mass with mullerian agenesis can be a diagnostic and management dilemma. Besides malignant ovarian tumor is rare in childhood, having concomitant mullerian anomaly which may contribute the development of neoplasm is rare finding.

Biography :

Email: gtesfaye14@yahoo.com